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Diseases of the eye and adnexa (H00-H59)

Note:: Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition

Excludes 2:: certain conditions originating in the perinatal period (P04-P96)
certain infectious and parasitic diseases (A00-B99)
complications of pregnancy, childbirth and the puerperium (O00-O9A)
congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
endocrine, nutritional and metabolic diseases (E00-E88)
injury (trauma) of eye and orbit (S05.-)
injury, poisoning and certain other consequences of external causes (S00-T88)
neoplasms (C00-D49)
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)

Disorders of choroid and retina (H30-H36)

H30

Chorioretinal inflammation [+]

H30.0

Focal chorioretinal inflammation [+]
Focal chorioretinitis
Focal choroiditis
Focal retinitis
Focal retinochoroiditis

H30.00

Unspecified focal chorioretinal inflammation [+]
Focal chorioretinitis NOS
Focal choroiditis NOS
Focal retinitis NOS
Focal retinochoroiditis NOS

H30.01

Focal chorioretinal inflammation, juxtapapillary [+]

H30.02

Focal chorioretinal inflammation of posterior pole [+]

H30.03

Focal chorioretinal inflammation, peripheral [+]

H30.04

Focal chorioretinal inflammation, macular or paramacular [+]

H30.1

Disseminated chorioretinal inflammation [+]
Disseminated chorioretinitis
Disseminated choroiditis
Disseminated retinitis
Disseminated retinochoroiditis

Excludes 2:

exudative retinopathy (H35.02-)

H30.10

Unspecified disseminated chorioretinal inflammation [+]
Disseminated chorioretinitis NOS
Disseminated choroiditis NOS
Disseminated retinitis NOS
Disseminated retinochoroiditis NOS

H30.11

Disseminated chorioretinal inflammation of posterior pole [+]

H30.12

Disseminated chorioretinal inflammation, peripheral [+]

H30.13

Disseminated chorioretinal inflammation, generalized [+]

H30.14

Acute posterior multifocal placoid pigment epitheliopathy [+]

H30.2

Posterior cyclitis [+]
Pars planitis

H30.8

Other chorioretinal inflammations [+]

H30.9

Unspecified chorioretinal inflammation [+]
Chorioretinitis NOS
Choroiditis NOS
Neuroretinitis NOS
Retinitis NOS
Retinochoroiditis NOS

H31

Other disorders of choroid [+]

H31.0

Chorioretinal scars [+]

Excludes 2:

postsurgical chorioretinal scars (H59.81-)

H31.00

Unspecified chorioretinal scars [+]

H31.01

Macula scars of posterior pole (postinflammatory) (post-traumatic) [+]

Excludes 1:

postprocedural choriorentinal scar (H59.81-)

H31.02

Solar retinopathy [+]

H31.09

Other chorioretinal scars [+]

H31.1

Choroidal degeneration [+]

Excludes 2:

angioid streaks of macula (H35.33)

H31.10

Unspecified choroidal degeneration [+]
Choroidal sclerosis NOS

H31.11

Age-related choroidal atrophy [+]

H31.12

Diffuse secondary atrophy of choroid [+]

H31.2

Hereditary choroidal dystrophy [+]

Excludes 2:

hyperornithinemia (E72.4)
ornithinemia (E72.4)

H31.3

Choroidal hemorrhage and rupture [+]

H31.30

Unspecified choroidal hemorrhage [+]

H31.31

Expulsive choroidal hemorrhage [+]

H31.32

Choroidal rupture [+]

H31.4

Choroidal detachment [+]

H31.40

Unspecified choroidal detachment [+]

H31.41

Hemorrhagic choroidal detachment [+]

H31.42

Serous choroidal detachment [+]

H31.8

Other specified disorders of choroid

H31.9

Unspecified disorder of choroid

H32

Chorioretinal disorders in diseases classified elsewhere

Code first	underlying disease, such as: congenital toxoplasmosis (P37.1) histoplasmosis (B39.-) leprosy (A30.-)
Excludes 1:	chorioretinitis (in): toxoplasmosis (acquired) (B58.01) tuberculosis (A18.53)

H33

Retinal detachments and breaks [+]

Excludes 1:

detachment of retinal pigment epithelium (H35.72-, H35.73-)

H33.0

Retinal detachment with retinal break [+]
Rhegmatogenous retinal detachment

Excludes 1:

serous retinal detachment (without retinal break) (H33.2-)

H33.00

Unspecified retinal detachment with retinal break [+]

H33.01

Retinal detachment with single break [+]

H33.02

Retinal detachment with multiple breaks [+]

H33.03

Retinal detachment with giant retinal tear [+]

H33.04

Retinal detachment with retinal dialysis [+]

H33.05

Total retinal detachment [+]

H33.1

Retinoschisis and retinal cysts [+]

Excludes 1:

congenital retinoschisis (Q14.1)
microcystoid degeneration of retina (H35.42-)

H33.10

Unspecified retinoschisis [+]

H33.11

Cyst of ora serrata [+]

H33.12

Parasitic cyst of retina [+]

H33.19

Other retinoschisis and retinal cysts [+]
Pseudocyst of retina

H33.2

Serous retinal detachment [+]
Retinal detachment NOS
Retinal detachment without retinal break

Excludes 1:

central serous chorioretinopathy (H35.71-)

H33.3

Retinal breaks without detachment [+]

Excludes 1:

chorioretinal scars after surgery for detachment (H59.81-)
peripheral retinal degeneration without break (H35.4-)

H33.30

Unspecified retinal break [+]

H33.31

Horseshoe tear of retina without detachment [+]
Operculum of retina without detachment

H33.32

Round hole of retina without detachment [+]

H33.33

Multiple defects of retina without detachment [+]

H33.4

Traction detachment of retina [+]
Proliferative vitreo-retinopathy with retinal detachment

H33.8

Other retinal detachments

H34

Retinal vascular occlusions [+]

Excludes 1:

amaurosis fugax (G45.3)

H34.0

Transient retinal artery occlusion [+]

H34.1

Central retinal artery occlusion [+]

H34.2

Other retinal artery occlusions [+]

H34.21

Partial retinal artery occlusion [+]
Hollenhorst's plaque
Retinal microembolism

H34.23

Retinal artery branch occlusion [+]

H34.8

Other retinal vascular occlusions [+]

H34.81

Central retinal vein occlusion [+]

One of the following 7th characters is to be assigned to codes in subcategory H34.81 to designate the severity of the occlusion:
0 - with macular edema
1 - with retinal neovascularization
2 - stable

H34.82

Venous engorgement [+]
Incipient retinal vein occlusion
Partial retinal vein occlusion

H34.83

Tributary (branch) retinal vein occlusion [+]

One of the following 7th characters is to be assigned to codes in subcategory H34.83 to designate the severity of the occlusion:
0 - with macular edema
1 - with retinal neovascularization
2 - stable

H34.9

Unspecified retinal vascular occlusion

H35

Other retinal disorders [+]

Excludes 2:

diabetic retinal disorders (E08.311-E08.359, E09.311-E09.359, E10.311-E10.359, E11.311-E11.359, E13.311-E13.359)

H35.0

Background retinopathy and retinal vascular changes [+]

Code also

any associated hypertension (I10)

H35.00

Unspecified background retinopathy

H35.01

Changes in retinal vascular appearance [+]
Retinal vascular sheathing

H35.02

Exudative retinopathy [+]
Coats retinopathy

H35.03

Hypertensive retinopathy [+]

H35.04

Retinal micro-aneurysms, unspecified [+]

H35.05

Retinal neovascularization, unspecified [+]

H35.06

Retinal vasculitis [+]
Eales disease
Retinal perivasculitis

H35.07

Retinal telangiectasis [+]

H35.09

Other intraretinal microvascular abnormalities
Retinal varices

H35.1

Retinopathy of prematurity [+]

H35.10

Retinopathy of prematurity, unspecified [+]
Retinopathy of prematurity NOS

H35.11

Retinopathy of prematurity, stage 0 [+]

H35.12

Retinopathy of prematurity, stage 1 [+]

H35.13

Retinopathy of prematurity, stage 2 [+]

H35.14

Retinopathy of prematurity, stage 3 [+]

H35.15

Retinopathy of prematurity, stage 4 [+]

H35.16

Retinopathy of prematurity, stage 5 [+]

H35.17

Retrolental fibroplasia [+]

H35.2

Other non-diabetic proliferative retinopathy [+]
Proliferative vitreo-retinopathy
Thalassemia proliferative retinopathy

Excludes 1:	proliferative vitreo-retinopathy with retinal detachment (H33.4-)
Excludes 2:	proliferative sickle-cell retinopathy (H36.82-)

H35.3

Degeneration of macula and posterior pole [+]

H35.30

Unspecified macular degeneration
Age-related macular degeneration

H35.31

Nonexudative age-related macular degeneration [+]
Atrophic age-related macular degeneration
Dry age-related macular degeneration

One of the following 7th characters is to be assigned to codes in subcategory H35.31 to designate the stage of the disease:
0 - stage unspecified
1 - early dry stage
2 - intermediate dry stage
3 - advanced atrophic without subfoveal involvement
4 - advanced atrophic with subfoveal involvement

H35.32

Exudative age-related macular degeneration [+]
Wet age-related macular degeneration

One of the following 7th characters is to be assigned to codes in subcategory H35.32 to designate the stage of the disease:
0 - stage unspecified
1 - with active choroidal neovascularization
2 - with inactive choroidal neovascularization
3 - with inactive scar

H35.33

Angioid streaks of macula

H35.34

Macular cyst, hole, or pseudohole [+]

H35.35

Cystoid macular degeneration [+]

Excludes 1:

cystoid macular edema following cataract surgery (H59.03-)

H35.36

Drusen (degenerative) of macula [+]

H35.37

Puckering of macula [+]

H35.38

Toxic maculopathy [+]

Code first	poisoning due to drug or toxin, if applicable (T36-T65 with fifth or sixth character 1-4)
Use additional	code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)

H35.4

Peripheral retinal degeneration [+]

Excludes 1:

hereditary retinal degeneration (dystrophy) (H35.5-)
peripheral retinal degeneration with retinal break (H33.3-)

H35.40

Unspecified peripheral retinal degeneration

H35.41

Lattice degeneration of retina [+]
Palisade degeneration of retina

H35.42

Microcystoid degeneration of retina [+]

H35.43

Paving stone degeneration of retina [+]

H35.44

Age-related reticular degeneration of retina [+]

H35.45

Secondary pigmentary degeneration [+]

H35.46

Secondary vitreoretinal degeneration [+]

H35.5

Hereditary retinal dystrophy [+]

Excludes 1:

dystrophies primarily involving Bruch's membrane (H31.1-)

H35.6

Retinal hemorrhage [+]

H35.7

Separation of retinal layers [+]

Excludes 1:

retinal detachment (serous) (H33.2-)
rhegmatogenous retinal detachment (H33.0-)

H35.70

Unspecified separation of retinal layers

H35.71

Central serous chorioretinopathy [+]

H35.72

Serous detachment of retinal pigment epithelium [+]

H35.73

Hemorrhagic detachment of retinal pigment epithelium [+]

H35.8

Other specified retinal disorders [+]

Excludes 2:

retinal hemorrhage (H35.6-)

H35.9

Unspecified retinal disorder

H36

Retinal disorders in diseases classified elsewhere [+]

Code first	underlying disease, such as: lipid storage disorders (E75.-) sickle-cell disorders (D57.-)
Excludes 1:	arteriosclerotic retinopathy (H35.0-) diabetic retinopathy (E08.3-, E09.3-, E10.3-, E11.3-, E13.3-)

H36.8

Other retinal disorders in diseases classified elsewhere [+]

H36.81

Nonproliferative sickle-cell retinopathy [+]

H36.82

Proliferative sickle-cell retinopathy [+]

H36.89

Other retinal disorders in diseases classified elsewhere
Retinal dystrophy in lipid storage disorders