Diseases of the nervous system (G00-G99)
Excludes 2:
certain conditions originating in the perinatal period (P04-P96) certain infectious and parasitic diseases (A00-B99) complications of pregnancy, childbirth and the puerperium (O00-O9A) congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) endocrine, nutritional and metabolic diseases (E00-E88) injury, poisoning and certain other consequences of external causes (S00-T88) neoplasms (C00-D49) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Diseases of myoneural junction and muscle (G70-G73)
G70
Myasthenia gravis and other myoneural disorders [+]
Excludes 1:
botulism (A05.1, A48.51-A48.52) transient neonatal myasthenia gravis (P94.0)
G70.0
Myasthenia gravis [+]
G70.00
Myasthenia gravis without (acute) exacerbation Myasthenia gravis NOS
G70.01
Myasthenia gravis with (acute) exacerbation Myasthenia gravis in crisis
G70.1
Toxic myoneural disorders
Code first
(T51-T65) to identify toxic agent
G70.2
Congenital and developmental myasthenia
G70.8
Other specified myoneural disorders [+]
G70.80
Lambert-Eaton syndrome, unspecified Lambert-Eaton syndrome NOS
G70.81
Lambert-Eaton syndrome in disease classified elsewhere
Code first
underlying disease
Excludes 1:
Lambert-Eaton syndrome in neoplastic disease (G73.1)
G70.89
Other specified myoneural disorders
G70.9
Myoneural disorder, unspecified
G71
Primary disorders of muscles [+]
Excludes 2:
arthrogryposis multiplex congenita (Q74.3) metabolic disorders (E70-E88) myositis (M60.-)
G71.0
Muscular dystrophy [+]
G71.00
Muscular dystrophy, unspecified
G71.01
Duchenne or Becker muscular dystrophy Autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker muscular dystrophy Benign [Becker] muscular dystrophy Severe [Duchenne] muscular dystrophy
G71.02
Facioscapulohumeral muscular dystrophy Scapulohumeral muscular dystrophy
G71.03
Limb girdle muscular dystrophies [+]
G71.031
Autosomal dominant limb girdle muscular dystrophy LGMD D4 calpain-3-related LGMD D5 collagen 6-related Limb girdle muscular dystrophy type 1
G71.032
Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction Limb girdle muscular dystrophy type 2A LGMD R1 calpain-3-related Primary calpainopathy
G71.033
Limb girdle muscular dystrophy due to dysferlin dysfunction Dysferlinopathy LGMD R2 dysferlin-related Limb girdle muscular dystrophy type 2B Miyoshi Myopathy type 1
G71.034
Limb girdle muscular dystrophy due to sarcoglycan dysfunction
G71.035
Limb girdle muscular dystrophy due to anoctamin-5 dysfunction Anoctamin-5-related LGMD R12 Anoctaminopathy Autosomal recessive limb girdle muscular dystrophy type 2L Miyoshi myopathy type 3
G71.038
Other limb girdle muscular dystrophy LGMD R9 FKRP-related LGMD R22 collagen 6-related Limb girdle muscular dystrophy due to fukutin related protein dysfunction Limb girdle muscular dystrophy type 2I Other autosomal recessive limb girdle muscular dystrophy
G71.039
Limb girdle muscular dystrophy, unspecified
G71.09
Other specified muscular dystrophies Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss] Congenital muscular dystrophy NOS Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber Distal muscular dystrophy Ocular muscular dystrophy Oculopharyngeal muscular dystrophy Scapuloperoneal muscular dystrophy
G71.1
Myotonic disorders [+]
G71.11
Myotonic muscular dystrophy Dystrophia myotonica [Steinert] Myotonia atrophica Myotonic dystrophy Proximal myotonic myopathy (PROMM) Steinert disease
G71.12
Myotonia congenita Acetazolamide responsive myotonia congenita Dominant myotonia congenita [Thomsen disease] Myotonia levior Recessive myotonia congenita [Becker disease]
G71.13
Myotonic chondrodystrophy Chondrodystrophic myotonia Congenital myotonic chondrodystrophy Schwartz-Jampel disease
G71.14
Drug induced myotonia
Use additional
code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
G71.19
Other specified myotonic disorders Myotonia fluctuans Myotonia permanens Neuromyotonia [Isaacs] Paramyotonia congenita (of von Eulenburg) Pseudomyotonia Symptomatic myotonia
G71.2
Congenital myopathies [+]
Excludes 2:
arthrogryposis multiplex congenita (Q74.3)
G71.20
Congenital myopathy, unspecified
G71.21
Nemaline myopathy
G71.22
Centronuclear myopathy [+]
G71.220
X-linked myotubular myopathy Myotubular (centronuclear) myopathy
G71.228
Other centronuclear myopathy Autosomal centronuclear myopathy Autosomal dominant centronuclear myopathy Autosomal recessive centronuclear myopathy Centronuclear myopathy, NOS
G71.29
Other congenital myopathy Central core disease Minicore disease Multicore disease Multiminicore disease
G71.3
Mitochondrial myopathy, not elsewhere classified
Excludes 1:
Kearns-Sayre syndrome (H49.81) Leber's disease (H47.21) Leigh's encephalopathy (G31.82) mitochondrial metabolism disorders (E88.4.-) Reye's syndrome (G93.7)
G71.8
Other primary disorders of muscles
G71.9
Primary disorder of muscle, unspecified Hereditary myopathy NOS
G72
Other and unspecified myopathies [+]
Excludes 1:
arthrogryposis multiplex congenita (Q74.3) dermatopolymyositis (M33.-) ischemic infarction of muscle (M62.2-) myositis (M60.-) polymyositis (M33.2.-)
G72.0
Drug-induced myopathy
Use additional
code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
G72.1
Alcoholic myopathy
Use additional
code to identify alcoholism (F10.-)
G72.2
Myopathy due to other toxic agents
Code first
(T51-T65) to identify toxic agent
G72.3
Periodic paralysis Familial periodic paralysis Hyperkalemic periodic paralysis (familial) Hypokalemic periodic paralysis (familial) Myotonic periodic paralysis (familial) Normokalemic paralysis (familial) Potassium sensitive periodic paralysis
Excludes 1:
paramyotonia congenita (of von Eulenburg) (G71.19)
G72.4
Inflammatory and immune myopathies, not elsewhere classified [+]
G72.41
Inclusion body myositis [IBM]
G72.49
Other inflammatory and immune myopathies, not elsewhere classified Inflammatory myopathy NOS
G72.8
Other specified myopathies [+]
G72.81
Critical illness myopathy Acute necrotizing myopathy Acute quadriplegic myopathy Intensive care (ICU) myopathy Myopathy of critical illness
G72.89
Other specified myopathies
G72.9
Myopathy, unspecified
G73
Disorders of myoneural junction and muscle in diseases classified elsewhere [+]
G73.1
Lambert-Eaton syndrome in neoplastic disease
Code first
underlying neoplasm (C00-D49)
Excludes 1:
Lambert-Eaton syndrome not associated with neoplasm (G70.80-G70.81)
G73.3
Myasthenic syndromes in other diseases classified elsewhere
Code first
underlying disease, such as: neoplasm (C00-D49) thyrotoxicosis (E05.-)
G73.7
Myopathy in diseases classified elsewhere
Code first
underlying disease, such as: glycogen storage disease (E74.0-) hyperparathyroidism (E21.0, E21.3) hypoparathyroidism (E20.-) lipid storage disorders (E75.-)
Excludes 1:
myopathy in: rheumatoid arthritis (M05.32) sarcoidosis (D86.87) scleroderma (M34.82) Sjögren syndrome (M35.03) systemic lupus erythematosus (M32.19)
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