Diseases of the nervous system (G00-G99)
Excludes 2:
certain conditions originating in the perinatal period (P04-P96) certain infectious and parasitic diseases (A00-B99) complications of pregnancy, childbirth and the puerperium (O00-O9A) congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99) endocrine, nutritional and metabolic diseases (E00-E88) injury, poisoning and certain other consequences of external causes (S00-T88) neoplasms (C00-D49) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Systemic atrophies primarily affecting the central nervous system (G10-G14)
G10
Huntington's disease Huntington's chorea Huntington's dementia
Use additional
code, if applicable, to identify:
Use additional
dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
Use additional
dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
Use additional
dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
Use additional
dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
Use additional
dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
Use additional
mild neurocognitive disorder due to known physiological condition (F06.7-)
G11
Hereditary ataxia [+]
Excludes 2:
cerebral palsy (G80.-) hereditary and idiopathic neuropathy (G60.-) metabolic disorders (E70-E88)
G11.0
Congenital nonprogressive ataxia
G11.1
Early-onset cerebellar ataxia [+]
G11.10
Early-onset cerebellar ataxia, unspecified
G11.11
Friedreich ataxia Autosomal recessive Friedreich ataxia Friedreich ataxia with retained reflexes
G11.19
Other early-onset cerebellar ataxia Early-onset cerebellar ataxia with essential tremor Early-onset cerebellar ataxia with myoclonus [Hunt's ataxia] Early-onset cerebellar ataxia with retained tendon reflexes X-linked recessive spinocerebellar ataxia
G11.2
Late-onset cerebellar ataxia
G11.3
Cerebellar ataxia with defective DNA repair Ataxia telangiectasia [Louis-Bar]
Excludes 2:
Cockayne's syndrome (Q87.19) other disorders of purine and pyrimidine metabolism (E79.-) xeroderma pigmentosum (Q82.1)
G11.4
Hereditary spastic paraplegia
G11.5
Hypomyelination - hypogonadotropic hypogonadism - hypodontia 4H syndrome Pol III-related leukodystrophy
G11.6
Leukodystrophy with vanishing white matter disease
G11.8
Other hereditary ataxias
G11.9
Hereditary ataxia, unspecified Hereditary cerebellar ataxia NOS Hereditary cerebellar degeneration Hereditary cerebellar disease Hereditary cerebellar syndrome
G12
Spinal muscular atrophy and related syndromes [+]
G12.0
Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
G12.1
Other inherited spinal muscular atrophy Adult form spinal muscular atrophy Childhood form, type II spinal muscular atrophy Distal spinal muscular atrophy Juvenile form, type III spinal muscular atrophy [Kugelberg-Welander] Progressive bulbar palsy of childhood [Fazio-Londe] Scapuloperoneal form spinal muscular atrophy
G12.2
Motor neuron disease [+]
G12.20
Motor neuron disease, unspecified
G12.21
Amyotrophic lateral sclerosis
G12.22
Progressive bulbar palsy
G12.23
Primary lateral sclerosis
G12.24
Familial motor neuron disease
G12.25
Progressive spinal muscle atrophy
G12.29
Other motor neuron disease
G12.8
Other spinal muscular atrophies and related syndromes
G12.9
Spinal muscular atrophy, unspecified
G13
Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere [+]
G13.0
Paraneoplastic neuromyopathy and neuropathy Carcinomatous neuromyopathy Sensorial paraneoplastic neuropathy [Denny Brown]
Code first
underlying neoplasm (C00-D49)
G13.1
Other systemic atrophy primarily affecting central nervous system in neoplastic disease Paraneoplastic limbic encephalopathy
Code first
underlying neoplasm (C00-D49)
G13.2
Systemic atrophy primarily affecting the central nervous system in myxedema
Code first
underlying disease, such as: hypothyroidism (E03.-) myxedematous congenital iodine deficiency (E00.1)
G13.8
Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere
Code first
underlying disease
G14
Postpolio syndrome
Includes:
postpolio myelitic syndrome
Excludes 1:
sequelae of poliomyelitis (B91)
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