| Q20 |
Congenital malformations of cardiac chambers and connections [+]
| Excludes 1: |
dextrocardia with situs inversus (Q89.3)
mirror-image atrial arrangement with situs inversus (Q89.3)
|
|
|
| Q20.0 |
Common arterial trunk
Persistent truncus arteriosus
| Excludes 1: |
aortic septal defect (Q21.4)
|
|
| Q20.1 |
Double outlet right ventricle
Taussig-Bing syndrome
|
| Q20.2 |
Double outlet left ventricle
|
| Q20.3 |
Discordant ventriculoarterial connection
Dextrotransposition of aorta
Transposition of great vessels (complete)
|
| Q20.4 |
Double inlet ventricle
Common ventricle
Cor triloculare biatriatum
Single ventricle
|
| Q20.5 |
Discordant atrioventricular connection
Corrected transposition
Levotransposition
Ventricular inversion
|
| Q20.6 |
Isomerism of atrial appendages
Isomerism of atrial appendages with asplenia or polysplenia
|
| Q20.8 |
Other congenital malformations of cardiac chambers and connections
Cor binoculare
|
| Q20.9 |
Congenital malformation of cardiac chambers and connections, unspecified
|
|
| Q21 |
Congenital malformations of cardiac septa [+]
| Excludes 1: |
acquired cardiac septal defect (I51.0)
|
|
|
| Q21.0 |
Ventricular septal defect
Roger's disease
|
| Q21.1 |
Atrial septal defect [+]
| Excludes 2: |
ostium primum atrial septal defect (type I) (Q21.20)
|
|
|
| Q21.10 |
Atrial septal defect, unspecified
|
| Q21.11 |
Secundum atrial septal defect
Fenestrated atrial septum
Patent or persistent ostium secundum defect (type II)
|
| Q21.12 |
Patent foramen ovale
Persistent foramen ovale
|
| Q21.13 |
Coronary sinus atrial septal defect
Coronary sinus defect
Unroofed coronary sinus
|
| Q21.14 |
Superior sinus venosus atrial septal defect
Superior vena cava type atrial septal defect
|
| Q21.15 |
Inferior sinus venosus atrial septal defect
Inferior vena cava type atrial septal defect
|
| Q21.16 |
Sinus venosus atrial septal defect, unspecified
Sinus venosus defect, NOS
|
| Q21.19 |
Other specified atrial septal defect
Common atrium
Other specified atrial septal abnormality
|
|
| Q21.2 |
Atrioventricular septal defect [+]
Atrioventricular canal defect
Endocardial cushion defect
Ostium primum atrial septal defect (type I)
|
|
| Q21.20 |
Atrioventricular septal defect, unspecified as to partial or complete
Atrioventricular canal, NOS
Endocardial cushion defect NOS
Ostium primum atrial septal defect (type I) NOS
|
| Q21.21 |
Partial atrioventricular septal defect
Incomplete atrioventricular canal
Incomplete atrioventricular septal defect
Incomplete endocardial cushion defect
Ostium primum atrial septal defect (type I) with separate atrioventricular valves
Partial atrioventricular canal
Partial endocardial cushion defect
|
| Q21.22 |
Transitional atrioventricular septal defect
Intermediate atrioventricular canal
Intermediate atrioventricular septal defect
Intermediate endocardial cushion defect
Ostium primum atrial septal defect (type I) with separate atrioventricular valves and a small or restrictive inlet VSD
Transitional atrioventricular canal
Transitional endocardial cushion defect
|
| Q21.23 |
Complete atrioventricular septal defect
Common atrioventricular canal
Common atrioventricular septal defect
Common endocardial cushion defect
Ostium primum atrial septal defect (type I) with common atrioventricular valve and a moderate or larger inlet VSD
|
|
| Q21.3 |
Tetralogy of Fallot
Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.
|
| Q21.4 |
Aortopulmonary septal defect
Aortic septal defect
Aortopulmonary window
|
| Q21.8 |
Other congenital malformations of cardiac septa
Eisenmenger's defect
Pentalogy of Fallot
| Code also |
, if applicable:
Eisenmenger's complex (I27.83)
Eisenmenger's syndrome (I27.83)
|
|
| Q21.9 |
Congenital malformation of cardiac septum, unspecified
Septal (heart) defect NOS
|
|
| Q22 |
Congenital malformations of pulmonary and tricuspid valves [+]
|
|
| Q22.0 |
Pulmonary valve atresia
|
| Q22.1 |
Congenital pulmonary valve stenosis
|
| Q22.2 |
Congenital pulmonary valve insufficiency
Congenital pulmonary valve regurgitation
|
| Q22.3 |
Other congenital malformations of pulmonary valve
Congenital malformation of pulmonary valve NOS
Supernumerary cusps of pulmonary valve
|
| Q22.4 |
Congenital tricuspid stenosis
Congenital tricuspid atresia
|
| Q22.5 |
Ebstein's anomaly
|
| Q22.6 |
Hypoplastic right heart syndrome
|
| Q22.8 |
Other congenital malformations of tricuspid valve
|
| Q22.9 |
Congenital malformation of tricuspid valve, unspecified
|
|
| Q23 |
Congenital malformations of aortic and mitral valves [+]
|
|
| Q23.0 |
Congenital stenosis of aortic valve
Congenital aortic atresia
Congenital aortic stenosis NOS
| Excludes 1: |
congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4)
congenital subaortic stenosis (Q24.4)
supravalvular aortic stenosis (congenital) (Q25.3)
|
|
| Q23.1 |
Congenital insufficiency of aortic valve
Congenital aortic insufficiency
|
| Q23.2 |
Congenital mitral stenosis
Congenital mitral atresia
|
| Q23.3 |
Congenital mitral insufficiency
|
| Q23.4 |
Hypoplastic left heart syndrome
|
| Q23.8 |
Other congenital malformations of aortic and mitral valves [+]
|
|
| Q23.81 |
Bicuspid aortic valve
Congenital bicuspid aortic valve
Unicuspid (congenital) aortic valve (at birth)
| Code also |
, if applicable, acquired aortic valve disorders, such as:
aortic (valve) insufficiency (nonrheumatic) (I35.1)
aortic (valve) stenosis (nonrheumatic) (I35.0)
aortic (valve) stenosis with insufficiency (nonrheumatic) (I35.2)
|
|
| Q23.82 |
Congenital mitral valve cleft leaflet
Cleft mitral valve leaflet at birth
|
| Q23.88 |
Other congenital malformations of aortic and mitral valves
|
|
| Q23.9 |
Congenital malformation of aortic and mitral valves, unspecified
|
|
| Q24 |
Other congenital malformations of heart [+]
| Excludes 1: |
endocardial fibroelastosis (I42.4)
|
|
|
| Q24.0 |
Dextrocardia
| Excludes 1: |
dextrocardia with situs inversus (Q89.3)
isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6)
mirror-image atrial arrangement with situs inversus (Q89.3)
|
|
| Q24.1 |
Levocardia
|
| Q24.2 |
Cor triatriatum
|
| Q24.3 |
Pulmonary infundibular stenosis
Subvalvular pulmonic stenosis
|
| Q24.4 |
Congenital subaortic stenosis
|
| Q24.5 |
Malformation of coronary vessels
Congenital coronary (artery) aneurysm
|
| Q24.6 |
Congenital heart block
|
| Q24.8 |
Other specified congenital malformations of heart
Congenital diverticulum of left ventricle
Congenital malformation of myocardium
Congenital malformation of pericardium
Malposition of heart
Uhl's disease
|
| Q24.9 |
Congenital malformation of heart, unspecified
Congenital anomaly of heart
Congenital disease of heart
|
|
| Q25 |
Congenital malformations of great arteries [+]
|
|
| Q25.0 |
Patent ductus arteriosus
Patent ductus Botallo
Persistent ductus arteriosus
|
| Q25.1 |
Coarctation of aorta
Coarctation of aorta (preductal) (postductal)
Stenosis of aorta
|
| Q25.2 |
Atresia of aorta [+]
|
|
| Q25.21 |
Interruption of aortic arch
Atresia of aortic arch
|
| Q25.29 |
Other atresia of aorta
Atresia of aorta
|
|
| Q25.3 |
Supravalvular aortic stenosis
| Excludes 1: |
congenital aortic stenosis NOS (Q23.0)
congenital stenosis of aortic valve (Q23.0)
|
|
| Q25.4 |
Other congenital malformations of aorta [+]
| Excludes 1: |
hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4)
|
|
|
| Q25.40 |
Congenital malformation of aorta unspecified
|
| Q25.41 |
Absence and aplasia of aorta
|
| Q25.42 |
Hypoplasia of aorta
|
| Q25.43 |
Congenital aneurysm of aorta
Congenital aneurysm of aortic root
Congenital aneurysm of aortic sinus
|
| Q25.44 |
Congenital dilation of aorta
|
| Q25.45 |
Double aortic arch
Vascular ring of aorta
|
| Q25.46 |
Tortuous aortic arch
Persistent convolutions of aortic arch
|
| Q25.47 |
Right aortic arch
Persistent right aortic arch
|
| Q25.48 |
Anomalous origin of subclavian artery
|
| Q25.49 |
Other congenital malformations of aorta
Aortic arch
Bovine arch
|
|
| Q25.5 |
Atresia of pulmonary artery
|
| Q25.6 |
Stenosis of pulmonary artery
Supravalvular pulmonary stenosis
|
| Q25.7 |
Other congenital malformations of pulmonary artery [+]
|
|
| Q25.71 |
Coarctation of pulmonary artery
|
| Q25.72 |
Congenital pulmonary arteriovenous malformation
Congenital pulmonary arteriovenous aneurysm
|
| Q25.79 |
Other congenital malformations of pulmonary artery
Aberrant pulmonary artery
Agenesis of pulmonary artery
Congenital aneurysm of pulmonary artery
Congenital anomaly of pulmonary artery
Hypoplasia of pulmonary artery
|
|
| Q25.8 |
Other congenital malformations of other great arteries
|
| Q25.9 |
Congenital malformation of great arteries, unspecified
|
|
| Q26 |
Congenital malformations of great veins [+]
|
|
| Q26.0 |
Congenital stenosis of vena cava
Congenital stenosis of vena cava (inferior)(superior)
|
| Q26.1 |
Persistent left superior vena cava
|
| Q26.2 |
Total anomalous pulmonary venous connection
Total anomalous pulmonary venous return [TAPVR], subdiaphragmatic
Total anomalous pulmonary venous return [TAPVR], supradiaphragmatic
|
| Q26.3 |
Partial anomalous pulmonary venous connection
Partial anomalous pulmonary venous return
|
| Q26.4 |
Anomalous pulmonary venous connection, unspecified
|
| Q26.5 |
Anomalous portal venous connection
|
| Q26.6 |
Portal vein-hepatic artery fistula
|
| Q26.8 |
Other congenital malformations of great veins
Absence of vena cava (inferior) (superior)
Azygos continuation of inferior vena cava
Persistent left posterior cardinal vein
Scimitar syndrome
|
| Q26.9 |
Congenital malformation of great vein, unspecified
Congenital anomaly of vena cava (inferior) (superior) NOS
|
|
| Q27 |
Other congenital malformations of peripheral vascular system [+]
| Excludes 2: |
anomalies of cerebral and precerebral vessels (Q28.0-Q28.3)
anomalies of coronary vessels (Q24.5)
anomalies of pulmonary artery (Q25.5-Q25.7)
congenital retinal aneurysm (Q14.1)
hemangioma and lymphangioma (D18.-)
|
|
|
| Q27.0 |
Congenital absence and hypoplasia of umbilical artery
Single umbilical artery
|
| Q27.1 |
Congenital renal artery stenosis
|
| Q27.2 |
Other congenital malformations of renal artery
Congenital malformation of renal artery NOS
Multiple renal arteries
|
| Q27.3 |
Arteriovenous malformation (peripheral) [+]
Arteriovenous aneurysm
| Excludes 1: |
acquired arteriovenous aneurysm (I77.0)
|
| Excludes 2: |
arteriovenous malformation of cerebral vessels (Q28.2)
arteriovenous malformation of precerebral vessels (Q28.0)
|
|
|
| Q27.30 |
Arteriovenous malformation, site unspecified
|
| Q27.31 |
Arteriovenous malformation of vessel of upper limb
|
| Q27.32 |
Arteriovenous malformation of vessel of lower limb
|
| Q27.33 |
Arteriovenous malformation of digestive system vessel
|
| Q27.34 |
Arteriovenous malformation of renal vessel
|
| Q27.39 |
Arteriovenous malformation, other site
|
|
| Q27.4 |
Congenital phlebectasia
|
| Q27.8 |
Other specified congenital malformations of peripheral vascular system
Absence of peripheral vascular system
Atresia of peripheral vascular system
Congenital aneurysm (peripheral)
Congenital stricture, artery
Congenital varix
| Excludes 1: |
arteriovenous malformation (Q27.3-)
|
|
| Q27.9 |
Congenital malformation of peripheral vascular system, unspecified
Anomaly of artery or vein NOS
|
|
| Q28 |
Other congenital malformations of circulatory system [+]
| Excludes 1: |
congenital aneurysm NOS (Q27.8)
congenital coronary aneurysm (Q24.5)
ruptured cerebral arteriovenous malformation (I60.8)
ruptured malformation of precerebral vessels (I72.0)
|
| Excludes 2: |
congenital peripheral aneurysm (Q27.8)
congenital pulmonary aneurysm (Q25.79)
congenital retinal aneurysm (Q14.1)
|
|
|
| Q28.0 |
Arteriovenous malformation of precerebral vessels
Congenital arteriovenous precerebral aneurysm (nonruptured)
|
| Q28.1 |
Other malformations of precerebral vessels
Congenital malformation of precerebral vessels NOS
Congenital precerebral aneurysm (nonruptured)
|
| Q28.2 |
Arteriovenous malformation of cerebral vessels
Arteriovenous malformation of brain NOS
Congenital arteriovenous cerebral aneurysm (nonruptured)
|
| Q28.3 |
Other malformations of cerebral vessels
Congenital cerebral aneurysm (nonruptured)
Congenital malformation of cerebral vessels NOS
Developmental venous anomaly
|
| Q28.8 |
Other specified congenital malformations of circulatory system
Congenital aneurysm, specified site NEC
Spinal vessel anomaly
|
| Q28.9 |
Congenital malformation of circulatory system, unspecified
|
|