| M30 |
Polyarteritis nodosa and related conditions [+]
| Excludes 1: |
microscopic polyarteritis (M31.7)
|
|
|
| M30.0 |
Polyarteritis nodosa
|
| M30.1 |
Polyarteritis with lung involvement [Churg-Strauss]
Allergic granulomatous angiitis
Eosinophilic granulomatosis with polyangiitis [EGPA]
|
| M30.2 |
Juvenile polyarteritis
|
| M30.3 |
Mucocutaneous lymph node syndrome [Kawasaki]
|
| M30.8 |
Other conditions related to polyarteritis nodosa
Polyangiitis overlap syndrome
|
|
| M31 |
Other necrotizing vasculopathies [+]
|
|
| M31.0 |
Hypersensitivity angiitis
Goodpasture's syndrome
|
| M31.1 |
Thrombotic microangiopathy [+]
|
|
| M31.10 |
Thrombotic microangiopathy, unspecified
|
| M31.11 |
Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]
Transplant-associated thrombotic microangiopathy [TA-TMA]
| Code first |
if applicable:
complications of bone marrow transplant (T86.0-)
complications of stem cell transplant (T86.5)
|
| Use additional |
code to identify specific organ dysfunction, such as: |
| Use additional |
acute kidney failure (N17.-) |
| Use additional |
acute respiratory distress syndrome (J80) |
| Use additional |
capillary leak syndrome (I78.8) |
| Use additional |
diffuse alveolar hemorrhage (R04.89) |
| Use additional |
encephalopathy (metabolic) (septic) (G93.41) |
| Use additional |
fluid overload, unspecified (E87.70) |
| Use additional |
graft versus host disease (D89.81-) |
| Use additional |
hemolytic uremic syndrome (D59.3-) |
| Use additional |
hepatic failure (K72.-) |
| Use additional |
hepatic veno-occlusive disease (K76.5) |
| Use additional |
idiopathic interstitial pneumonia (J84.11-) |
| Use additional |
sinusoidal obstruction syndrome (K76.5) |
|
| M31.19 |
Other thrombotic microangiopathy
Thrombotic thrombocytopenic purpura
|
|
| M31.2 |
Lethal midline granuloma
|
| M31.3 |
Wegener's granulomatosis [+]
Granulomatosis with polyangiitis
Necrotizing respiratory granulomatosis
|
|
| M31.30 |
Wegener's granulomatosis without renal involvement
Wegener's granulomatosis NOS
|
| M31.31 |
Wegener's granulomatosis with renal involvement
|
|
| M31.4 |
Aortic arch syndrome [Takayasu]
|
| M31.5 |
Giant cell arteritis with polymyalgia rheumatica
|
| M31.6 |
Other giant cell arteritis
|
| M31.7 |
Microscopic polyangiitis
Microscopic polyarteritis
| Excludes 1: |
polyarteritis nodosa (M30.0)
|
|
| M31.8 |
Other specified necrotizing vasculopathies
Hypocomplementemic vasculitis
Septic vasculitis
|
| M31.9 |
Necrotizing vasculopathy, unspecified
|
|
| M32 |
Systemic lupus erythematosus (SLE) [+]
| Excludes 1: |
lupus erythematosus (discoid) (NOS) (L93.0)
|
|
|
| M32.0 |
Drug-induced systemic lupus erythematosus
| Use additional |
code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5) |
|
| M32.1 |
Systemic lupus erythematosus with organ or system involvement [+]
|
|
| M32.10 |
Systemic lupus erythematosus, organ or system involvement unspecified
|
| M32.11 |
Endocarditis in systemic lupus erythematosus
Libman-Sacks disease
|
| M32.12 |
Pericarditis in systemic lupus erythematosus
Lupus pericarditis
|
| M32.13 |
Lung involvement in systemic lupus erythematosus
Pleural effusion due to systemic lupus erythematosus
|
| M32.14 |
Glomerular disease in systemic lupus erythematosus
Lupus renal disease NOS
|
| M32.15 |
Tubulo-interstitial nephropathy in systemic lupus erythematosus
|
| M32.19 |
Other organ or system involvement in systemic lupus erythematosus
| Use additional |
code(s) to identify organ or system involvement, such as encephalitis (G05.3) |
|
|
| M32.8 |
Other forms of systemic lupus erythematosus
|
| M32.9 |
Systemic lupus erythematosus, unspecified
SLE NOS
Systemic lupus erythematosus NOS
Systemic lupus erythematosus without organ involvement
|
|
| M33 |
Dermatopolymyositis [+]
|
|
| M33.0 |
Juvenile dermatomyositis [+]
|
|
| M33.00 |
Juvenile dermatomyositis, organ involvement unspecified
|
| M33.01 |
Juvenile dermatomyositis with respiratory involvement
|
| M33.02 |
Juvenile dermatomyositis with myopathy
|
| M33.03 |
Juvenile dermatomyositis without myopathy
|
| M33.09 |
Juvenile dermatomyositis with other organ involvement
|
|
| M33.1 |
Other dermatomyositis [+]
Adult dermatomyositis
|
|
| M33.10 |
Other dermatomyositis, organ involvement unspecified
|
| M33.11 |
Other dermatomyositis with respiratory involvement
|
| M33.12 |
Other dermatomyositis with myopathy
|
| M33.13 |
Other dermatomyositis without myopathy
Dermatomyositis NOS
|
| M33.19 |
Other dermatomyositis with other organ involvement
|
|
| M33.2 |
Polymyositis [+]
|
|
| M33.20 |
Polymyositis, organ involvement unspecified
|
| M33.21 |
Polymyositis with respiratory involvement
|
| M33.22 |
Polymyositis with myopathy
|
| M33.29 |
Polymyositis with other organ involvement
|
|
| M33.9 |
Dermatopolymyositis, unspecified [+]
|
|
| M33.90 |
Dermatopolymyositis, unspecified, organ involvement unspecified
|
| M33.91 |
Dermatopolymyositis, unspecified with respiratory involvement
|
| M33.92 |
Dermatopolymyositis, unspecified with myopathy
|
| M33.93 |
Dermatopolymyositis, unspecified without myopathy
|
| M33.99 |
Dermatopolymyositis, unspecified with other organ involvement
|
|
|
| M34 |
Systemic sclerosis [scleroderma] [+]
| Excludes 1: |
circumscribed scleroderma (L94.0)
neonatal scleroderma (P83.88)
|
|
|
| M34.0 |
Progressive systemic sclerosis
|
| M34.1 |
CR(E)ST syndrome
Combination of calcinosis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, telangiectasia
|
| M34.2 |
Systemic sclerosis induced by drug and chemical
| Code first |
poisoning due to drug or toxin, if applicable (T36-T65 with fifth or sixth character 1-4)
|
| Use additional |
code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5) |
|
| M34.8 |
Other forms of systemic sclerosis [+]
|
|
| M34.81 |
Systemic sclerosis with lung involvement
| Code also |
if applicable:
other interstitial pulmonary diseases (J84.89)
secondary pulmonary arterial hypertension (I27.21)
|
|
| M34.82 |
Systemic sclerosis with myopathy
|
| M34.83 |
Systemic sclerosis with polyneuropathy
|
| M34.89 |
Other systemic sclerosis
|
|
| M34.9 |
Systemic sclerosis, unspecified
|
|
| M35 |
Other systemic involvement of connective tissue [+]
| Excludes 1: |
reactive perforating collagenosis (L87.1)
|
|
|
| M35.0 |
Sjögren syndrome [+]
Sicca syndrome
| Use additional |
code to identify associated manifestations |
| Excludes 1: |
dry mouth, unspecified (R68.2)
|
|
|
| M35.00 |
Sjögren syndrome, unspecified
|
| M35.01 |
Sjögren syndrome with keratoconjunctivitis
|
| M35.02 |
Sjögren syndrome with lung involvement
|
| M35.03 |
Sjögren syndrome with myopathy
|
| M35.04 |
Sjögren syndrome with tubulo-interstitial nephropathy
Renal tubular acidosis in sicca syndrome
|
| M35.05 |
Sjögren syndrome with inflammatory arthritis
|
| M35.06 |
Sjögren syndrome with peripheral nervous system involvement
|
| M35.07 |
Sjögren syndrome with central nervous system involvement
|
| M35.08 |
Sjögren syndrome with gastrointestinal involvement
|
| M35.0A |
Sjögren syndrome with glomerular disease
|
| M35.0B |
Sjögren syndrome with vasculitis
|
| M35.0C |
Sjögren syndrome with dental involvement
|
| M35.09 |
Sjögren syndrome with other organ involvement
|
|
| M35.1 |
Other overlap syndromes
Mixed connective tissue disease
| Excludes 1: |
polyangiitis overlap syndrome (M30.8)
|
|
| M35.2 |
Behçet's disease
|
| M35.3 |
Polymyalgia rheumatica
| Excludes 1: |
polymyalgia rheumatica with giant cell arteritis (M31.5)
|
|
| M35.4 |
Diffuse (eosinophilic) fasciitis
|
| M35.5 |
Multifocal fibrosclerosis
|
| M35.6 |
Relapsing panniculitis [Weber-Christian]
| Excludes 1: |
lupus panniculitis (L93.2)
panniculitis NOS (M79.3-)
|
|
| M35.7 |
Hypermobility syndrome
Familial ligamentous laxity
| Excludes 1: |
ligamentous laxity, NOS (M24.2-)
|
| Excludes 2: |
Ehlers-Danlos syndromes (Q79.6-)
|
|
| M35.8 |
Other specified systemic involvement of connective tissue [+]
|
|
| M35.81 |
Multisystem inflammatory syndrome
MIS-A
MIS-C
Multisystem inflammatory syndrome in adults
Multisystem inflammatory syndrome in children
Pediatric inflammatory multisystem syndrome
PIMS
| Code first |
, if applicable, COVID-19 (U07.1)
|
| Code also |
any associated complications such as:
acute hepatic failure (K72.0-)
acute kidney failure (N17.-)
acute myocarditis (I40.-)
acute respiratory distress syndrome (J80)
cardiac arrhythmia (I47-I49.-)
pneumonia due to COVID-19 (J12.82)
severe sepsis (R65.2-)
viral cardiomyopathy (B33.24)
viral pericarditis (B33.23)
|
| Use additional |
code, if applicable, for: |
| Use additional |
exposure to COVID-19 or SARS-CoV-2 infection (Z20.822) |
| Use additional |
personal history of COVID-19 (Z86.16) |
| Use additional |
post COVID-19 condition (U09.9) |
|
| M35.89 |
Other specified systemic involvement of connective tissue
|
|
| M35.9 |
Systemic involvement of connective tissue, unspecified
Autoimmune disease (systemic) NOS
Collagen (vascular) disease NOS
|
|
| M36 |
Systemic disorders of connective tissue in diseases classified elsewhere [+]
| Excludes 2: |
arthropathies in diseases classified elsewhere (M14.-)
|
|
|
| M36.0 |
Dermato(poly)myositis in neoplastic disease
| Code first |
underlying neoplasm (C00-D49)
|
|
| M36.1 |
Arthropathy in neoplastic disease
| Code first |
underlying neoplasm, such as:
leukemia (C91-C95)
malignant histiocytosis (C96.A)
multiple myeloma (C90.0)
|
|
| M36.2 |
Hemophilic arthropathy
Hemarthrosis in hemophilic arthropathy
| Code first |
underlying disease, such as:
factor VIII deficiency (D66)
with vascular defect (D68.0-)
factor IX deficiency (D67)
hemophilia (classical) (D66)
hemophilia B (D67)
hemophilia C (D68.1)
|
|
| M36.3 |
Arthropathy in other blood disorders
|
| M36.4 |
Arthropathy in hypersensitivity reactions classified elsewhere
| Code first |
underlying disease, such as:
Henoch (-Schönlein) purpura (D69.0)
serum sickness (T80.6-)
|
|
| M36.8 |
Systemic disorders of connective tissue in other diseases classified elsewhere
| Code first |
underlying disease, such as:
alkaptonuria (E70.29)
hypogammaglobulinemia (D80.-)
ochronosis (E70.29)
|
|
|